A case report of hemophagocytic lymphohistiocytosis (HLH).
نویسندگان
چکیده
Hemophagocytic lymphohistiocytosis (HLH), is an uncommon, life-threatening hyperinflammatory syndrome caused by severe hypercytokinemia with excessive activation of lymphocytes and macrophages due to a highly stimulated but ineffective immune process. We report a case of Hemophagocytic Lymphohistiocytosis in a 15 year old boy presenting with fever, lymphadenopathy and pancytopenia due to infection caused by Klebsiella Pneumoniae and Acinetobacter.
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عنوان ژورنال:
- The Journal of the Association of Physicians of India
دوره 62 7 شماره
صفحات -
تاریخ انتشار 2014